Cystic fibrosis yog qhov qub txeeg qub teg, ua rau muaj kev phom sij rau lub neej uas ua rau lub ntsws thiab lub plab zom mov. Nws yog tshwm sim los ntawm kev hloov pauv caj ces uas nres koj lub ntsws, txiav, thiab lwm yam kabmob los ntawm kev ua haujlwm raws li qhov lawv yuav tsum tau ua. Qhov no tsim cov hnoos qeev uas thaiv cov kab mob pancreatic ducts, hnyuv, thiab bronchi, ua rau muaj kab mob ua pa thiab teeb meem zom zaub mov. Qhov teeb meem no tuaj yeem kuaj pom los ntawm kev kuaj ntshav, kuaj tawm hws, lossis kuaj lub ntsws, lossis los ntawm kev xoo hluav taws xob hauv siab. Yog tias koj cev xeeb tub thiab muaj caj ces muaj feem rau qhov teeb meem no, koj tseem tuaj yeem txiav txim siab kuaj cev xeeb tub kom pom tias koj tus menyuam muaj kev pheej hmoo.
Cov kauj ruam
Txoj Kev 1 ntawm 5: Paub txog Cov tsos mob ntawm Cystic Fibrosis
Kauj Ruam 1. Saib rau hws qab ntsev hauv cov menyuam
Ntau tus menyuam yaus nrog cystic fibrosis yuav muaj hws qab ntsev heev. Koj yuav pom nws thaum koj hnia koj tus menyuam.
Cov menyuam yaus nrog cystic fibrosis yuav tsis pom txhua tus tsos mob ntawm tus kabmob mus txog thaum lawv laus lossis lawv cov tsos mob yuav mob zuj zus ntxiv thaum lawv hnub nyoog
Kauj Ruam 2. Saib cov teeb meem ua pa xws li hawb pob thiab hnoos tsis tu ncua
Yog tias koj muaj cystic fibrosis, koj yuav ntsib teeb meem ua pa xws li hawb pob, ua tsis taus pa, hnoos tsis tu ncua uas ua rau hnoos qeev, thiab mob ntsws.
Koj kuj tseem tuaj yeem muaj teeb meem rov tshwm sim xws li mob ntsws, mob ntsws, lossis mob ntsws. Cov no feem ntau pib thaum tseem hluas
Kauj Ruam 3. Tshaj tawm yog tias koj muaj cem quav hnyav thiab quav quav tsw tsw
Cystic fibrosis tuaj yeem ua rau koj lub plab zom zaub mov kom tsis ua haujlwm, ua rau muaj teeb meem xws li hnyuv txhaws, teeb meem quav, thiab quav quav lossis quav tsw tsw.
Kauj Ruam 4. Mus kuaj yog tias koj muaj caj ces predisposition
Qee tus neeg muaj cov noob tsis xws uas tuaj yeem ua rau lawv muaj kev pheej hmoo loj hlob ntawm cystic fibrosis. Yog cystic fibrosis khiav hauv koj tsev neeg, koj yuav tsum tau kuaj rau qhov tsis meej pem no. Kev kuaj mob ntxov tuaj yeem pab ua kom koj lub neej zoo dua qub thiab muab rau koj nkag mus rau cov kev kho mob zoo.
Koj tus kws kho mob yuav qhia ua qhov kev kuaj ntshav txhawm rau txheeb xyuas yog tias koj muaj cov noob tsis zoo uas tuaj yeem txuas nrog cystic fibrosis
Txoj Kev 2 ntawm 5: Ua Ntsuas Ntshav rau Cystic Fibrosis
Kauj Ruam 1. Cia koj tus kws kho mob kuaj ntshav
Cov menyuam mos thiab cov laus tuaj yeem kuaj mob nrog cystic fibrosis siv cov qauv ntshav. Koj tus kws kho mob yuav hnia koj cov ntiv tes thiab kuaj ntshav ntawm daim npav.
Yog tias koj tus kws kho mob tab tom kuaj tus menyuam yug tshiab, lawv yuav coj mus kuaj thaum tus menyuam muaj hnub nyoog 5-8 hnub los ntawm kev txhuam lawv ko taw
Kauj Ruam 2. Tau kuaj cov ntshav mus rau qib siab ntawm cov tshuaj tiv thaiv kab mob trypsinogen
Tus kws kho mob yuav saib kom siab dua qib ib txwm ntawm cov tshuaj hu ua immunoreactive trypsinogen (IRT) hauv koj cov ntshav. Cov tshuaj no tau tso tawm los ntawm koj cov txiav txiav thiab ntau dhau ntawm nws tuaj yeem yog lub cim qhia tias koj cov txiav txiav tsis ua haujlwm zoo.
Kauj Ruam 3. Cia koj tus kws kho mob kuaj cov ntshav kom pom tias muaj cov kab mob tsis zoo
Yog tias koj xav tias koj tus menyuam yuav muaj cystic fibrosis, koj tus kws kho mob yuav kuaj koj cov ntshav mus kuaj rau cov noob tsis zoo uas tuaj yeem ua rau cystic fibrosis los tsim hauv koj cov xeeb ntxwv. Cov nqa khoom feem ntau tsis tsim cov kab mob cystic fibrosis, tab sis lawv yuav kis cov noob tsis raug rau lawv cov menyuam, ua rau lawv muaj kev pheej hmoo loj ntawm kev tsim teeb meem.
Koj tus kws kho mob tuaj yeem hais qhia kom tau txais kev kuaj ntshav nqa cov noob yog tias koj tab tom txiav txim siab muaj menyuam lossis yog cystic fibrosis khiav hauv koj tsev neeg
Txoj Kev 3 ntawm 5: Tau Txais Kev Ntshav Qab Zib rau Cystic Fibrosis
Kauj Ruam 1. Kom koj tus kws kho mob ua qhov ntsuas hws
Koj tus kws kho mob yuav xa cov cuab yeej nrog tshuaj lom neeg thiab hluav taws xob rau koj lub xub pwg lossis koj tus ncej puab. Tom qab ntawd lawv yuav sau hws ntawm ib daim ntawv lim los yog daim ntaub qhwv rau kev sim.
- Cov menyuam mos yug los tsis tuaj yeem kuaj mob cystic fibrosis siv qhov ntsuas tawm hws mus txog thaum lawv muaj hnub nyoog tsawg kawg 3-4 lub lis piam.
- Tsis txhob siv cov tshuaj pleev lossis tshuaj pleev rau 24 teev ua ntej kuaj hws.
Kauj Ruam 2. Tau kuaj koj cov hws mus kuaj kom pom cov tshuaj chloride siab
Yog tias koj muaj cov tshuaj chloride ntau dua 60 mmol/L, koj yuav muaj cystic fibrosis.
Koj qhov kev kuaj hws kuj tseem tuaj yeem cim "txawv txav" yog tias koj tus kws kho mob xav tias koj muaj cystic fibrosis
Kauj Ruam 3. Kom kuaj hws ua ob zaug kom paub tseeb tias kuaj mob
Yog tias koj cov qauv hws rov qab txawv txav, koj tus kws kho mob yuav ua nws dua. Yog tias koj qhov kev sim zaum thib ob rov qab txawv txav, lawv yuav lees tias koj muaj cystic fibrosis.
Yog tias koj qhov kev sim zaum thib ob tsis rov qab txawv txav, lawv tuaj yeem kuaj ntshav lossis kuaj ntshav tawm kom paub tseeb tias koj kuaj mob
Txoj Kev 4 ntawm 5: Muaj Kev Xeem Prenatal rau Cystic Fibrosis
Kauj Ruam 1. Xav txog kev kuaj cev xeeb tub yog tias koj cev xeeb tub thiab muaj caj ces ua rau mob qog noj ntshav
Koj tus kws kho mob yuav pom zoo kom koj kuaj ua ntej yug menyuam rau cystic fibrosis yog tias qhov teeb meem tshwm sim hauv koj tsev neeg lossis yog tias koj yog tus nqa cov noob tsis zoo uas ua rau nws. Qhov kev xeem feem ntau yog qhov tseeb thiab tuaj yeem qhia koj yog tias koj tus menyuam cov noob yog ib txwm muaj lossis yog tias lawv muaj kev pheej hmoo ntawm kev tsim cystic fibrosis. Txawm li cas los xij, xeem qhov no yog qhov kev txiav txim siab tus kheej uas koj yuav tsum tau tham nrog koj tus kws kho mob thiab koj lwm qhov tseem ceeb, yog tias lawv koom nrog.
Tham txog qhov zoo thiab qhov tsis zoo nrog koj tus kws kho mob thiab qhia koj tus kheej ua ntej koj txiav txim siab ua qhov kev xeem
Kauj Ruam 2. Txiav txim siab tso cai rau koj tus kws kho mob tshem dej tawm ntawm koj lub hnab amniotic
Koj tus kws kho mob yuav muab rab koob tso rau hauv koj lub plab phab ntsa thiab tom qab ntawd nkag rau hauv koj lub tsev menyuam. Lawv yuav rho me me ntawm cov kua los ntawm lub hnab amniotic, uas yog lub hnab uas nyob ib puag ncig koj tus menyuam.
Qhov kev xeem no tuaj yeem ua tiav ntawm koj tus kws kho mob lub chaw haujlwm thiab yuav tsum tsis txhob mob siab rau koj
Kauj Ruam 3. Tham nrog koj tus kws kho mob txog kev coj mus kuaj ntawm koj tus placenta
Lwm qhov kev kuaj cev xeeb tub cuam tshuam nrog kws kho mob ua lub raj nyias rau hauv koj lub paum thiab lub ncauj tsev menyuam kom txog thaum nws mus txog qhov tso menyuam. Tom qab ntawd lawv yuav nqus ib qho piv txwv ntawm cov placenta rau kev sim.
Kev nqus siv yuav ua rau maj mam thiab yuav tsum tsis txhob mob lossis tsis xis nyob rau koj
Txoj Kev 5 ntawm 5: Tau X-Ray Hauv Siab thiab Kuaj Ntshav
Kauj Ruam 1. Cia koj tus kws kho mob xoo hluav taws xob hauv koj lub hauv siab
Xoo hluav taws hauv siab tuaj yeem pab koj tus kws kho mob pom yog tias muaj thaj tsam ntawm koj lub ntsws uas tau mob o lossis mob caws pliav. Lawv kuj tseem tuaj yeem nrhiav cov cim qhia huab cua hauv koj lub ntsws. Cov no yog txhua qhov ua tau pom ntawm cystic fibrosis.
Kauj Ruam 2. Ua qhov kev ntsuas lub ntsws ua haujlwm
Koj tus kws kho mob yuav kom koj ua qhov kev ntsuas ua pa, uas ntsuas koj lub ntsws lub peev xwm los pauv cov pa thiab carbon dioxide kom raug. Koj yuav tsum ua pa mus rau hauv lub tshuab tshwj xeeb los ua cov kev ntsuas no.
Kauj Ruam 3. Ua kom tiav cov kev ntsuas ntawm cov kua hauv koj lub ntsws
Koj tus kws kho mob yuav ua qhov ntsuas kab mob hnoos qeev, uas ntsuas cov kua uas koj hnoos los ntawm koj lub ntsws. Lawv tuaj yeem qhia qhov kev xeem no yog tias koj muaj teeb meem ntsws lossis koj twb tau pom cov tsos mob ntawm cystic fibrosis.