Yuav Kho Li Cas Mast Cell Activation Syndrome

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Yuav Kho Li Cas Mast Cell Activation Syndrome
Yuav Kho Li Cas Mast Cell Activation Syndrome

Video: Yuav Kho Li Cas Mast Cell Activation Syndrome

Video: Yuav Kho Li Cas Mast Cell Activation Syndrome
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Cia peb ntsib nws: tsis muaj leej twg nyiam ua xua. Tab sis yog tias koj tau txais mast cell activation syndrome (MCAS), koj tuaj yeem ntsib cov tsos mob ua xua tsis muaj laj thawj hlo li. Hmoov zoo, muaj kev kho mob los pab koj tswj hwm koj cov tsos mob.

Cov kauj ruam

Lo lus nug 1 ntawm 6: Tom Qab

Kho Mast Cell Activation Syndrome Kauj Ruam 1
Kho Mast Cell Activation Syndrome Kauj Ruam 1

Kauj Ruam 1. Mast cell tso cov kws kho nruab nrab uas ua rau muaj kev tsis haum tshuaj

Mast cells yeej yog ib feem tseem ceeb ntawm koj lub cev tiv thaiv kab mob. Thaum twg koj raug mob lossis raug rau lub cev txawv teb chaws (zoo li ua xua), koj lub cell mast tso cov tshuaj hu ua kws kho nruab nrab uas pab tiv thaiv thiab kho koj lub cev. Histamine yog ib qho piv txwv qub ntawm tus kws kho mob tso tawm los ntawm koj lub cell mast uas pab tiv thaiv kev ua xua.

Kho Mast Cell Activation Syndrome Kauj Ruam 2
Kho Mast Cell Activation Syndrome Kauj Ruam 2

Kauj Ruam 2. MCAS ua rau koj lub cell mast tso cov kws kho nruab nrab yam tsis muaj laj thawj

Thaum koj muaj MCAS, koj lub cell mast puas lawm thiab cov kws kho nruab nrab lawv tso tawm tuaj yeem ua rau muaj kev tsis haum tshuaj. Qee zaum, koj lub xov tooj ntawm tes tuaj yeem tsim cov xov tooj cua zoo ib yam (hu ua clones) uas tom qab ntawd tsim tawm ntau dua lossis tso tawm cov kws kho nruab nrab.

Lo lus nug 2 ntawm 6: Ua rau

Kho Mast Cell Activation Syndrome Kauj Ruam 3
Kho Mast Cell Activation Syndrome Kauj Ruam 3

Kauj Ruam 1. Qhov tseeb ua rau tsis paub, tab sis MCAS tuaj yeem yog caj ces

Lub sijhawm MCAS, qhov uas koj pom cov tsos mob ntawm kev tsis haum tshuaj, hu ua "idiopathic." Qhov ntawd txhais tau tias nws tsis tau tshwm sim lossis tshwm sim los ntawm ib yam dab tsi thiab tsuas yog tshwm sim tshwm sim. Txawm li cas los xij, cov kev tshawb fawb qhia tias yuav muaj kev tshuaj ntsuam caj ces rau MCAS, thiab koj muaj feem yuav muaj nws yog tias koj muaj ib tus txheeb ze uas muaj nws.

Kho Mast Cell Activation Syndrome Kauj Ruam 4
Kho Mast Cell Activation Syndrome Kauj Ruam 4

Kauj Ruam 2. Kab mob Lyme tuaj yeem ua rau MCAS

Kab mob Lyme yog tshwm sim los ntawm cov kab mob uas kis tau rau tib neeg los ntawm zuam kis. Cov tsos mob ntawm tus kab mob Lyme suav nrog ua npaws, mob taub hau, qaug zog, thiab cov yam ntxwv ntawm daim tawv nqaij hu ua erythema migrans. Ntau tus neeg mob Lyme tsim kev tsis haum tshuaj hnyav rau cov zaub mov, tshuaj noj, thiab tshuaj lom neeg, uas tuaj yeem yog tus cim ntawm MCAS.

Nqe lus nug 3 ntawm 6: Cov tsos mob

Kho Mast Cell Activation Syndrome Kauj Ruam 5
Kho Mast Cell Activation Syndrome Kauj Ruam 5

Kauj Ruam 1. MCAS ua rau khaus khaus, o, ua pa nyuaj, thiab raws plab

Cov tsos mob ntawm ntu MCAS zoo ib yam zoo ib yam rau kev ua xua. Cov kws kho mob nruab nrab tso tawm los ntawm koj cov kab mob mast tuaj yeem cuam tshuam rau koj cov tawv nqaij, lub plab zom mov, thiab koj cov pa ua pa.

Kho Mast Cell Activation Syndrome Kauj Ruam 6
Kho Mast Cell Activation Syndrome Kauj Ruam 6

Kauj Ruam 2. Koj tseem tuaj yeem muaj lub plawv dhia nrawm thiab ntshav siab

Qhov MCAS rov tuaj yeem ua rau muaj kev cuam tshuam hauv koj cov hlab plawv, ua rau koj lub plawv dhia nrawm dua. Koj kuj tseem tuaj yeem ua rau cov ntshav siab poob qis, uas tuaj yeem ua rau koj nkees nkees, ua rau pom kev, lossis zoo li koj yuav tsaus muag. Yog tias koj cov ntshav siab poob qis txaus, koj tuaj yeem tawm mus.

Nqe lus nug 4 ntawm 6: Kev kuaj mob

Kho Mast Cell Activation Syndrome Kauj Ruam 7
Kho Mast Cell Activation Syndrome Kauj Ruam 7

Kauj Ruam 1. Tus kws kho mob tshwj xeeb hauv MCAS yuav tsum tau kuaj mob

Vim tias MCAS yog qhov tshiab thiab tsis nkag siab zoo, tsis muaj ntau qhov kev sim uas tuaj yeem lees paub qhov kev kuaj mob. Hloov chaw, tus kws kho mob uas paub txog tus mob tuaj yeem tshuaj xyuas thiab ntsuas koj li keeb kwm kev kho mob txhawm rau kuaj mob. Yog tias koj tus kws kho mob tsis tuaj yeem kuaj mob rau koj, lawv tuaj yeem xa koj mus rau tus kws tshaj lij uas tuaj yeem ua tau.

Kho Mast Cell Activation Syndrome Kauj Ruam 8
Kho Mast Cell Activation Syndrome Kauj Ruam 8

Kauj Ruam 2. Kev kuaj ua xua tuaj yeem txiav tawm qhov tsis haum

Yog tias koj tseem muaj cov tsos mob ntawm kev tsis haum tshuaj, koj tus kws kho mob yuav xa koj mus rau tus ua xua. Lawv tuaj yeem kuaj koj rau ntau yam kev ua xua sib txawv. Yog tias tsis muaj qhov tsis haum rau koj cov tsos mob, koj yuav muaj MCAS.

Nqe lus nug 5 ntawm 6: Kev Kho Mob

Kho Mast Cell Activation Syndrome Kauj Ruam 9
Kho Mast Cell Activation Syndrome Kauj Ruam 9

Kauj Ruam 1. Cov tshuaj ua xua pab txo koj cov tsos mob

Vim tias cov tsos mob tam sim ntawm MCAS rov zoo ib yam li kev ua xua, cov tshuaj ua xua tuaj yeem pab txo qis thiab tswj hwm lawv. Antihistamines tuaj yeem pab ua rau khaus, tsis xis nyob hauv plab, thiab yaug tawm. Epinephrine tuaj yeem pab yog tias koj ua pa nyuaj.

Kho Mast Cell Activation Syndrome Kauj Ruam 10
Kho Mast Cell Activation Syndrome Kauj Ruam 10

Kauj Ruam 2. Corticosteroids tau siv los kho qhov mob hnyav

Lawv tuaj yeem pab nrog mob hnyav ntawm khaus, ua pa nyuaj, thiab o loj, hu ua edema. Tab sis, lawv tsuas yog siv los ua qhov kawg, yog li koj tus kws kho mob feem ntau tsuas yog sau ntawv rau lawv yog tias koj cov tsos mob hnyav.

Kho Mast Cell Activation Syndrome Kauj Ruam 11
Kho Mast Cell Activation Syndrome Kauj Ruam 11

Kauj Ruam 3. Omalizumab yuav pab tswj koj li MCAS

Omalizumab yog tshuaj tshwj xeeb uas siv los kho mob hawb pob hnyav. Cov kev tshawb fawb qhia tias kev txhaj tshuaj tsawg (li 150 mg ib hlis) zoo li muaj txiaj ntsig zoo ntawm kev tswj hwm MCAS thiab tiv thaiv kev mob hnyav.

Kho Mast Cell Activation Syndrome Kauj Ruam 12
Kho Mast Cell Activation Syndrome Kauj Ruam 12

Kauj Ruam 4. Tsis txhob ua tej yam uas ua rau koj cov tsos mob los pab tiv thaiv kab mob

Cov txhais yog cov tshuaj tshwj xeeb lossis cov tshuaj uas tuaj yeem ua rau koj lub cell mast tso cov kws kho mob nruab nrab. Nws tuaj yeem yog yam xws li zaub mov tshwj xeeb, tsw ntxhiab, lossis txias txias. Taug qab txhua yam uas ua rau koj muaj cov tsos mob ua xua. Sim zam txhua yam uas koj paub yuav ua rau ntu ntu zoo li koj tuaj yeem ua tau.

Nqe lus nug 6 ntawm 6: Kev kwv yees

  • Kho Mast Cell Activation Syndrome Kauj Ruam 13
    Kho Mast Cell Activation Syndrome Kauj Ruam 13

    Kauj Ruam 1. Tswj koj cov tsos mob yog txoj hauv kev zoo tshaj plaws los daws nrog MCAS

    Thaum tseem tsis tau paub kho rau MCAS, muaj cov tshuaj uas koj tuaj yeem siv los pab daws thiab tswj koj cov tsos mob. Muaj MCAS txhais tau tias koj yuav muaj kev pheej hmoo siab ntau rau kev ua xua, yuav ua rau muaj kev phom sij rau lub neej uas tuaj yeem tshwm sim yog tias koj li MCAS ua rau muaj kev cuam tshuam loj heev. Yog tias koj tuaj yeem zam qhov tshwm sim thiab tswj hwm koj cov tsos mob, koj tuaj yeem tiv thaiv kev mob anaphylaxis thiab txo qis MCAS ntu.

    Lub tswv yim

    Ua raws txhua yam uas ua rau muaj MCAS rov qab yog li koj tuaj yeem sim zam lawv yav tom ntej

    Lus ceeb toom

    • Yog tias koj muaj teeb meem ua pa lossis koj cov tsos mob ua xua hnyav dhau, nrhiav kev kho mob xwm txheej ceev.
    • Tsis txhob noj tshuaj yuav tshuaj tshwj tsis yog koj tus kws kho mob tau sau tseg.
  • Pom zoo: