Yuav kuaj li cas Hemophilia: 9 Kauj Ruam (nrog Duab)

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Yuav kuaj li cas Hemophilia: 9 Kauj Ruam (nrog Duab)
Yuav kuaj li cas Hemophilia: 9 Kauj Ruam (nrog Duab)

Video: Yuav kuaj li cas Hemophilia: 9 Kauj Ruam (nrog Duab)

Video: Yuav kuaj li cas Hemophilia: 9 Kauj Ruam (nrog Duab)
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Hemophilia yog teeb meem caj ces uas tib neeg cov ntshav tsis txhaws vim tsis muaj cov ntshav khov. Nws feem ntau dhau los ntawm niam txiv mus rau menyuam tab sis tuaj yeem tshwm sim ntawm nws tus kheej vim yog kev hloov pauv caj ces. Hemophilia feem ntau kuaj pom thaum tseem me. Yog tias koj lossis koj tus menyuam tab tom los ntshav ntau dhau, thiab cov ntshav los siv sijhawm ntev los nres, ces hemophilia yuav yog qhov ua rau. Txhawm rau kom tau txais kev kuaj mob kom raug, koj yuav tsum txheeb xyuas cov tsos mob thiab yam tseem ceeb thiab tom qab ntawd mus rau kws kho mob kom kuaj mob.

Cov kauj ruam

Ntu 1 ntawm 3: Txheeb Xyuas Cov Cim Qhia ntawm Hemophilia

Ntsuam xyuas Hemophilia Kauj Ruam 1
Ntsuam xyuas Hemophilia Kauj Ruam 1

Kauj Ruam 1. Txheeb xyuas cov teeb meem nrog ntshav ntau dhau thiab tsis muaj ntshav khov

Cov tsos mob tseem ceeb ntawm hemophilia yog tias koj muaj lub sijhawm nyuaj los ntshav tom qab koj pib los ntshav. Kev txhaws ntshav tsis feem ntau tshwm sim tam sim ntawd tab sis yog tias koj txiav me me los yog qhov ntswg me me nws yuav tsum pib li ob peb feeb. Yog tias koj tsis tuaj yeem zoo li tau txiav me me kom tsis txhob los ntshav, ces koj yuav muaj hemophilia.

Txhawm rau txiav kom tsis txhob los ntshav, siv qhov siab rau nws nrog cov ntaub qhwv tsis huv. Thaum cov ntshav los qeeb, tsis txhob muab daim ntaub qhwv tawm. Cias txuas ntxiv qhov siab thiab khaws cov ntaub qhwv kom lub cev tsis rub tawm qhov raug mob

Kuaj Kab Mob Hemophilia Kauj Ruam 2
Kuaj Kab Mob Hemophilia Kauj Ruam 2

Kauj Ruam 2. Xav txog kev pheej hmoo caj ces

Txij li hemophilia yog teeb meem caj ces, nws feem ntau kis los ntawm niam txiv mus rau menyuam. Yog tias koj niam koj txiv muaj hemophilia, koj muaj kev pheej hmoo kis tus kab mob ntau dua. Ib qho ntxiv, hemophilia tshwm sim hauv cov txiv neej ntau dua li poj niam.

  • Nug koj niam koj txiv yog tias lawv muaj nws lossis yog ib tus ntawm lawv cov txheeb ze muaj nws. Muaj ntau zaus, koj yuav tau paub yog tias koj niam koj txiv muaj hemophilia. Yog tias lawv ua, koj muaj feem yuav muaj nws.
  • Hemophilia yog kev hloov pauv uas tshwm sim ntawm X-chromosome. Txiv neej muaj X thiab Y chromosomes, thiab poj niam muaj ob X chromosomes. Qhov no txhais tau tias kom muaj hemophilia, txiv neej tsuas xav tau ib qho kev hloov pauv hauv X chromosome hos cov poj niam xav tau ob-ib qho ntawm txhua X chromosome. Yog li thaum hemophilia tshwm sim ntau zaus hauv txiv neej ntau dua poj niam, poj niam tuaj yeem nqa cov noob thiab xa mus rau lawv cov tub.
Kuaj Kab Mob Hemophilia Kauj Ruam 3
Kuaj Kab Mob Hemophilia Kauj Ruam 3

Kauj Ruam 3. Txiav tawm lwm yam uas tuaj yeem ua rau cov ntshav nyias nyias

Muaj qee qhov laj thawj koj yuav los ntshav ntau heev uas tsis muaj dab tsi ua nrog hemophilia. Ua ntej koj xav tias koj muaj tus mob no, koj yuav tsum txiav tawm lwm yam ua rau.

  • Piv txwv li, yog tias koj tab tom noj tshuaj anticoagulant, uas txwv tsis pub khov, koj yuav los ntshav ntev dua. Muaj ntau yam tshuaj uas tuaj yeem ua rau koj cov ntshav nyias thiab tiv thaiv koj lub peev xwm los khov, suav nrog warfarin (Coumadin, enoxaparin (Lovenox), clopidogrel (Plavix), ticlopidine (Ticlid), tshuaj aspirin, thiab NSAIDS, xws li Ibuprofen. Lwm hom tshuaj anticoagulants suav nrog qhov Xa Xa inhibitors (Xarelto, Eliquis, Arixtra) thiab thrombin inhibitors (Angiomax, Pradaxa). Tham nrog koj tus kws kho mob lossis tus kws muag tshuaj txog seb cov tshuaj uas koj noj yuav ua rau koj cov ntshav qis thiab txwv tsis pub khov.
  • Yog tias koj muaj ntshav los piav tsis tau nws tuaj yeem yog los ntawm cov zaub mov uas muaj salicylate, uas ib txwm ua rau cov ntshav, lossis txawm tias haus cawv ntau dhau. Kev siv cov qej ntau, qej, roj ntses, thiab cov tshuaj vitamin E kuj tseem tuaj yeem ua cov tshuaj tiv thaiv kab mob.

Ntu 2 ntawm 3: Tau Txais Kev Tshawb Fawb Tshwj Xeeb

Kuaj Kab Mob Hemophilia Kauj Ruam 4
Kuaj Kab Mob Hemophilia Kauj Ruam 4

Kauj Ruam 1. Teem caij nrog koj tus kws kho mob

Yog tias koj txhawj xeeb tias koj yuav muaj hemophilia, tom qab ntawd koj yuav tsum sab laj nrog koj tus kws kho mob txog nws. Tsis txhob xav tias koj tuaj yeem tswj ntshav me ntsis ntau dhau ntawm koj tus kheej. Hemophilia yuav tsum tau tswj hwm kev kho mob, yog li tau txais kev kuaj mob thiab phiaj xwm kho mob.

Hemophilia tuaj yeem yog tus mob hnyav heev, yog li thaum koj hu mus rau lub sijhawm teem qhia cov kws kho mob tias koj xav li cas. Lawv yuav tsum coj koj mus ntsib kws kho mob sai

Kuaj Kab Mob Hemophilia Kauj Ruam 5
Kuaj Kab Mob Hemophilia Kauj Ruam 5

Kauj Ruam 2. Tham nrog koj tus kws kho mob

Piav koj cov tsos mob thiab vim li cas koj thiaj xav tias lawv yuav cuam tshuam nrog hemophilia. Npaj los tham txog lwm qhov laj thawj uas ua rau muaj ntshav ntau dhau nrog koj tus kws kho mob.

  • Yog tias koj nqa hemophilia nrog koj tus kws kho mob lawv yuav muaj peev xwm ua keeb kwm tsev neeg ntau nrog koj txhawm rau txheeb xyuas yog tias koj muaj keeb kwm ntawm tus mob hauv koj tsev neeg. Qhov no yog vim qhov xwm txheej tau txuas nrog rau kev muaj caj ces.
  • Sau tag nrho koj cov tsos mob thiab thaum lawv tshwm sim ua ntej koj mus rau kws kho mob lub chaw haujlwm. Nqa cov npe ntawd nrog koj thaum koj mus ntsib kws kho mob. Cov tsos mob suav nrog cov pos hniav los ntshav, tso zis tsaus nti, ntshav hauv qhov ntswg, ntshav hauv cov quav, thiab ua kom tawv nqaij yooj yim.
Kuaj Kab Mob Hemophilia Kauj Ruam 6
Kuaj Kab Mob Hemophilia Kauj Ruam 6

Kauj Ruam 3. Muaj kev xeem tiav

Yog tias koj tus kws kho mob xav tias yuav tsum tau lees paub, koj yuav tau kuaj ntsuas los ntsuas seb koj cov ntshav khov sai npaum li cas, koj qib ntawm cov ntshav txhaws li cas, thiab seb koj puas muaj cov ntshav txhaws tag nrho. Kev ntsuam xyuas yuav qhia seb koj puas muaj hemophilia, yam koj muaj, thiab mob hnyav npaum li cas.

  • Kev kuaj mob hemophilia yuav tsum tau kuaj ntshav. Kev kuaj ntshav saib qib qib VIII thiab qhov tseem ceeb IX hauv cov ntshav, uas yog cov ntshav txhaws hauv cov ntshav.
  • Yog thawj qhov kev kuaj ntshav qhia pom qib qis ntawm cov ntshav txhaws, tom qab ntawd koj tus kws kho mob yuav muaj feem yuav mus rau kev tshuaj ntsuam caj ces txhawm rau txheeb xyuas qhov hloov pauv hemophilia.
  • Muaj ob hom hemophilia. Hom A, uas suav txog kwv yees li 80% ntawm cov neeg mob, yog qhov tsis txaus ntawm cov ntshav coagulation VIII thaum Hom B yog qhov tsis muaj ntshav khov ntau IX. Ob leeg muaj cov tsos mob zoo ib yam, tab sis kev kuaj ntshav tuaj yeem txiav txim siab seb koj muaj hom twg.

Ntu 3 ntawm 3: Nyob Nrog Hemophilia

Kuaj Kab Mob Hemophilia Kauj Ruam 7
Kuaj Kab Mob Hemophilia Kauj Ruam 7

Kauj Ruam 1. Tau txais kev kho mob tsim nyog

Thaum koj tau kuaj pom tus mob hemophilia koj yuav tsum tau txais kev kho mob rau tus kab mob. Hemophilia tuaj yeem ua rau muaj ntshav ntau dhau sab nraud thiab sab hauv lub cev, yog li kev kho mob tseem ceeb rau koj kev noj qab haus huv.

  • Kev kho mob tseem ceeb rau hemophilia yog kev hloov kho. Qhov no yog txheej txheem uas tib neeg cov ntshav los ntawm cov neeg pub dawb tau ua tiav thiab tau tshem nws cov ntshav khov. Cov txheej txheem khov no tau muab tso rau hauv cov ntshav hemophiliac.
  • Kev hloov pauv tuaj yeem ua tiav tas li los tiv thaiv ntshav hauv cov neeg uas muaj hemophilia hnyav. Nws kuj tseem tuaj yeem siv ib zaug ib ntus kom tsis txhob los ntshav hauv cov neeg uas muaj mob hnyav.
Kuaj Kab Mob Hemophilia Kauj Ruam 8
Kuaj Kab Mob Hemophilia Kauj Ruam 8

Kauj Ruam 2. Hloov txoj kev ua neej

Thaum koj kuaj pom tus mob hemophilia nws tseem ceeb heev uas koj yuav tsum hloov pauv hauv koj lub neej uas yuav tiv thaiv teeb meem ntshav. Ntxiv rau kev kho mob, koj yuav tsum zam kev ua ub no uas tuaj yeem ua rau koj lub cev raug mob thiab zam kev siv tshuaj thiab zaub mov uas tuaj yeem txhawb kev ntshav.

  • Kev ceev faj kom tsis txhob raug mob yog ib feem loj ntawm cov kev hloov pauv uas yuav xav tau. Zam kev ua kis las lossis cov dej num uas tuaj yeem ua rau nqaij tawv lossis txiav. Rau hemophiliac, cov khoom no tuaj yeem ua rau muaj kev phom sij rau lub neej.
  • Kuj tsis txhob noj tshuaj lossis noj zaub mov uas tuaj yeem ua rau cov ntshav tsawg. Cov tshuaj uas ua rau cov ntshav muaj xws li NSAIDS (ibuprofen), tshuaj aspirin, thiab anticoagulants, xws li warfarin. Cov zaub mov uas tuaj yeem ua rau cov ntshav, suav nrog qej thiab qhiav.
Kuaj Kab Mob Hemophilia Kauj Ruam 9
Kuaj Kab Mob Hemophilia Kauj Ruam 9

Kauj Ruam 3. Saib xyuas qhov xwm txheej

Ua raws li koj tus kws kho mob txoj phiaj xwm kho mob, suav nrog tau txais kev kho mob hloov pauv, thiab nco ntsoov tau txais kev saib xyuas mob tas li thiab tshuaj xyuas. Yog tias koj muaj hemophilia, nws yog ib qho tseem ceeb uas koj yuav tsum tau ua raws koj tus mob, es tsis txhob quav ntsej nws thiab vam tias nws yuav ploj mus ntawm nws tus kheej.

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